Table 2 β and α-glucosidase activities of human controls and Gaucher disease fibroblasts
From: Assessment of cellular cobalamin metabolism in Gaucher disease
Cell lines | β-glucosidase activity (nmol/mLxh) | α-glucosidase activity (nmol/mLxh) | ||
|---|---|---|---|---|
Without HOCbl | With HOCbl | Without HOCbl | With HOCbl | |
NHDF | 31.2 | 22.2 | 84.8 | 126.3 |
HFF | 27.6 | 26.9 | 70.6 | 79.1 |
Control-W | 18.7 | 21.8 | 101.0 | 106.6 |
GM00852 (GD I) | ND | ND | 102.3 | 61.4 |
GM00877 (GD II) | ND | ND | 92.1 | 147.8 |
GM20272 (GD III) | ND | ND | 104.9 | 150.7 |
GM00878 (RecNciI/−) | 30.9 | 29.3 | 134.7 | 72.4 |