No.* | Indiv. | Sex | Age | Age at first presentation (Diagnosis) | ECG*** | Echo | MRI | |||
---|---|---|---|---|---|---|---|---|---|---|
MWT † (mm) | LVEF ‡ | MWT † (mm) | LVEF (%) | Late enhancement | ||||||
1 | II-3§ | m | 56 | 49 (HCM) | SR, CV | 28 | n | 27 | 60 | mid-, inferoseptal and inferior basal |
II-9 | m | 55 | 53 (HCM) | AF, LBBB | 30 | n-↓ | 33 | 51 | massive septal, anterior, inferior | |
2 | II-1§ | m | 55 | 55 (HCM) | pxAF | 24 | n | |||
III-1 | f | 30 | 30|| (HCM) | SR | 15 | n | ||||
3 | SP# | m | 71 | 67 (HCM) | AF | 20 | n-↓ | |||
4 | SP# | m | 48 | 46 (HCM) | SR, CV, iLBBB | 25 | ↓ | |||
5 | I-2 | f | 85 | n.a. (-) | AF | 11 | n | |||
II-2§ | m | 65 | 62 (DCM) | SR, CV | 15†† | n | 12.5 | 72‡‡ | discrete septal (mid and basal) | |
II-6 | f | 55 | 55|| (-) | SR | 10 | n | < 11 | 65 | none | |
III-2 | m | 38 | 38 (susp.) | SR | 14†† | n | < 11 | 62§S | none | |
6 | II-2 | f | 68 | n.a. (HCM) | SR | n.a. | ||||
III-1§ | m | 39 | 18 (HCM) | SR | n.a. | |||||
7 | SP# | f | 52 | 45 (HCM) | SR, CV | n.a. | n | |||
8 | I-2 | f | 71 | 69|| (HCM) | SR | 20 | n | |||
II-1§ | m | 49 | 35 (HCM) | SR, AVB1, pxAF | 25 | ↓ | 26 | 71 | n.a. | |
9 | SP# | f | 66 | 44 (HCM) | SR, pxAF | 24 | n | |||
10 | SP# | m | 54 | 54 (HCM) | SR | 22 | n | |||
11 | II-3 | m | 66 | 66|| (HCM) | AF | 20 | n | |||
II-6§ | f | 62 | 54 (HCM) | SR | 22 | n-↓ | ||||
12 | II-6 | m | 67 | 67|| (susp.) | SR, LAHB | 12 | n | |||
III-1 | m | 46 | 42|| (HCM) | SR | 14 | n | 21 | 54 | massive intramural basal- and mid-septal | |
III-3§ | m | 42 | 37 (HCM) | SR | 30 | n | ||||
IV-4 | f | 20 | 20|| (HCM) | SR | 14 | n | 14 | 77 | none | |
IV-5 | f | 14 | 14|| (susp.) | SR | 13 | n | 11 | 66 | none | |
13 | II-1 | m | 54 | 54 (HCM) | SR | 13 | n | |||
II-6§ | m | 42 | 21 (HCM) | SR | 27 | ↓ | ||||
14 | II-2§ | f | 61 | 57 (HCM) | SR | 14|| | n | |||
II-5 | m | 55 | 55|| (HCM) | SR | 18 | n | 20 | 74 | mid and basal septal | |
15 | SP# | m | 49 | 49 (HCM) | SR | 19 | n | 24 | 62 | anteroseptal basal |
16 | II-3§ | m | 66## | 57 (DCM) | AF | n.a.## | ↓↓↓## | |||
II-5 | m | 65 | 34 (DCM) | AF, LBBB | 12 | ↓↓↓ | ||||
III-3 | m | 42 | 18 (HCM) | SR | 15 | n | 22 | 67 | intense septal | |
III-6 | f | 40 | 40|| (HCM) | SR | 15 | n | ||||
III-7 | f | 39 | 39|| (HCM) | SR | 15 | n | 14.5 | 72 | septal, inferoseptal basal | |
III-9 | f | 44 | 44|| (HCM) | SR, iLBBB | 16 | n | 22 | 71 | midseptal and inferoseptal basal | |
17 | II-3§ | m | 72 | n.a. (HCM) | AF, RBBB | 16 | n | |||
III-6 | m | 48 | n.a. (HCM) | SR | 24 | n | ||||
III-8 | f | 43 | 43|| (HCM) | SR | 10 | n | 13.5 | 65 | discrete basal-septal | |
III-9 | m | 42 | 42|| (HCM) | SR | 18 | n | ||||
IV-2 | m | 17 | 17|| (susp.) | SR | 12 | n | ||||
18 | II-4§ | f | 37 | 27 (HCM) | SR | 23 | n | 24 | 66 | massive intramural basal- and mid-septal |
III-5 | m | 15 | 15|| (susp.) | SR | 12 | n |